Le cuivre est nécessaire au fonctionnement de l’organisme. Il est d’ailleurs présent dans une grande partie de notre alimentation. Le cuivre produit par la nourriture est stocké dans le foie.

Le pronostic de la maladie de Wilson est habituellement bon, sauf en cas de maladie avancée avant le début du traitement.

Le traitement de la maladie de Wilson passe par notamment par le suivi d’un régime alimentaire pauvre en cuivre et la prise de médicaments à vie. 

Sunflower cataract and thick KF ring of the forty-12 months-outdated male with Wilson's disease and decompensated Long-term liver disease

  Cette greffe permet au affected individual de retrouver un foie sain et un fonctionnement hépatique convenable, sans pour autant le guérir de la maladie de Wilson.

On assessment, indications of Persistent liver disease for instance spider angiomata (small distended blood vessels, typically to the upper body) might be observed. Long-term Lively hepatitis has currently triggered cirrhosis with the liver for most patients by the time they build signs or symptoms. Though most people with cirrhosis have an increased danger of hepatocellular carcinoma (liver cancer), this threat is comparatively very low in Wilson's disease.[five]

The most crucial web pages of copper accumulation are the liver and Mind. Therefore, liver disease and neuropsychiatric symptoms are the main features that cause prognosis.[5] People with liver problems are likely to return for professional medical notice before (commonly as little ones or young adults) than Individuals with neurological and psychiatric signs and symptoms, who tend to be of their 20s or older.

De réduire au most les apports en cuivre dans l’alimentation du chien et de favoriser l’excrétion du cuivre.

La maladie de Wilson est une maladie génétique secondaire liée à une accumulation de cuivre dans l'organisme et se manifestant par des atteintes du foie et du système nerveux.

Introduction: Wilson’s disease, or hepatolenticular degeneration, was to start with described in 1912 because of the neurologist S.A.K. Wilson as being a consistently mortal familial disease characterised by neurological impairment connected with cirrhosis. That is a rare autosomal recessive genetic disease, leading to abnormalities of your copper copyright ATP7B. The disease is characterized by absolutely free copper accumulation in tissues; mostly while in the liver, the Mind and also the cornea. Considering that 1956 people have benefited from a highly effective cure having a copper-chelating agent, D-penicillamine, that restrictions the consequences from the disease.

Our articles or blog posts and contents are for academic applications only. With any well being linked subject talked over on This website you should not rely upon any info on this site as an alternative for professional health care analysis, treatment, suggestions, or in its place for, Specialist counseling care, tips, treatment, or diagnosis.

Some are discovered only for the reason that kin are diagnosed with Wilson's disease; numerous of these, when analyzed, transform out to are enduring signs on the ailment but haven't received a diagnosis.[six]

Parlant de la maladie de Wilson, c’est une maladie héréditaire uncommon. Elle rend la tache difficile au foie qui n’élimine plus l’excès de cuivre dans la bile comme cela se doit normalement.

Les maladie de wilson personnes touchées par cette maladie doivent prendre des médicaments pour éliminer le cuivre et éviter de consommer des aliments à haute teneur en cuivre pour le restant de leur vie.